Xeroderma Pigmentosum: Relato de Dois Casos

Authors

  • Liliane D. Herter Doutoranda. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Nilton T. Herter Professor Adjunto do Departamento de Cirurgia e Chefe do Serviço de Cabeça e Pescoço. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Paulo Roberto Ferreira Godoy Pós-Graduando. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Nelson Heller Serviço de Cirurgia Plástica. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Níveo Steffen Serviço de Cirurgia Plástica. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Rosaura Hartmann Serviço de Dermatologia. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil
  • Milton Luis Luswanberg Serviço de Pediatria. Fundação Faculdade Federal de Ciências Médicas e Hospital Santa Rita. Porto Alegre (RS), Brasil

DOI:

https://doi.org/10.32635/2176-9745.RBC.1986v32n2.3247

Keywords:

Skin Cancer, Prevenrion of Skin Cancer

Abstract

Xeroderma pigmentosum is a rare, serious and hereditarian disease. The diagnosis is essentially clinical. So far, there is not a completely efficacious therapy. Based on these facts, the authors review me literature concerning the etiology, etiopathogenesis and pathology of me condition. They report two cases treated in the Hospital Santa Rita of Associação Sulriograndense de Combate ao Câncer emphasizing the clinical and surgical treatment of the disease, and its precancerous and cancerous lesions.

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References

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Published

2023-08-07

How to Cite

1.
Herter LD, Herter NT, Godoy PRF, Heller N, Steffen N, Hartmann R, Luswanberg ML. Xeroderma Pigmentosum: Relato de Dois Casos. Rev. Bras. Cancerol. [Internet]. 2023 Aug. 7 [cited 2024 Jun. 30];32(2):127-32. Available from: https://rbc.inca.gov.br/index.php/revista/article/view/3247

Issue

Section

CASE REPORT