Primary Solitary Fibrous Tumor in Pelvic Region: Case Report
DOI:
https://doi.org/10.32635/2176-9745.RBC.2022v68n4.2560Keywords:
solitary fibrous tumors, pelvic neoplasms, case reportsAbstract
Introduction: Solitary fibrous tumor is a rare mesenchymal neoplasm, originated from CD34-positive interstitial dendritic cells and composed by the juxtaposition of spindle cells. Initial cases were primarily described in the thoracic region, the main site being the visceral pleura. However, cases of solitary extra-pleural fibrous tumors have already been described in the pelvic region demonstrating the possibility of multiple primary sites. Case report: A 38-year-old female patient, previously healthy and asymptomatic, seeks medical advice after a routine pelvic ultrasound that showed a heterogeneous image in the right adnexal region, paraovarian, being submitted to surgical resection of the lesion with a diagnosis of solitary fibrous tumor confirmed by immunohistochemistry. Aspects of immunohistochemical diagnosis and surgical treatment were discussed. Conclusion: Cases of solitary fibrous tumor in the pelvic region can be discovered through routine pelvic ultrasound. Surgical treatment, with extended resection and negative margins, should be the main objective in cases of solitary fibrous tumor in the pelvic region. Obtaining samples for immunohistochemical analysis is recommended and positivity for CD34 and STAT6 discloses the diagnosis. Relapses can occur in up to a decade of follow-up, and a long period of post-surgical follow-up is recommended.
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