Sclerosing epitelioid fibrosarcoma: case report and review of the literature

Authors

  • Patrícia Patury Borba Ex-residente do INCA. Médica do Serviço de Ginecologia Oncológica do HC-II - INCA.
  • Nelson Jabour Fiod Médico do Serviço de Tecido Ósseo e Conectivo do HC I - INCA
  • Gustavo de Castro Gouveia Médico residente em Cirurgia Oncológica do INCA
  • Marilene F. Nascimento Médica do Serviço de Anatomia Patológica do INCA
  • José Francisco de Rezende Chefe da Seção de Tecido Ósseo e Conectivo do INCA

DOI:

https://doi.org/10.32635/2176-9745.RBC.2003v49n4.2075

Keywords:

Sclerosing Epitelioid Fibrossarcoma, Soft Tissue Sarcoma, Diagnosis, Surgery

Abstract

The sclerosing epitelioid fibrossarcoma (SEF) is a malignant neoplasm made by nests and cords of small round cells, with clear cytoplasm, exuberant hyalinization and a high degree of necrosis. It seldom occurs in the limbs, trunk and neck. The SEF is a low degree tumor, and is reative to p53. Local recurrence is related to close resection margins. Differencial diagnosis includes nodular fascitis, desmoids tumor, fibrous hystiocitoma, synovial fibrossarcoma, clear cell sarcoma and alveolar rabdomiossarcoma. Tumor size, trunk localization and gender (male) compromises diagnosis. The autors relat a 44 years old patient case, with tumor in the middle anterior portion of the right forearm, and biopsy confirming SEF. Histology, clinical presentation and management options are discussed.

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Published

2003-12-30

How to Cite

1.
Borba PP, Fiod NJ, Gouveia G de C, Nascimento MF, Rezende JF de. Sclerosing epitelioid fibrosarcoma: case report and review of the literature. Rev. Bras. Cancerol. [Internet]. 2003 Dec. 30 [cited 2024 Nov. 22];49(4):221-5. Available from: https://rbc.inca.gov.br/index.php/revista/article/view/2075

Issue

Vol. 49 No. 4 (2003): Oct./Nov./Dec.

Section

CASE REPORT

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