Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review

Authors

  • Cecília M. L. Costa Pediatra-Oncologista, titular do Departamento de Pediatria do Hospital do Câncer.
  • Patricia Rondinelli Residente de oncologia pediátrica do Departamento de Pediatria do Hospital do Câncer.
  • Beatriz de Camargo Pediatra-Oncologista, Doutora em Medicina - FMUSP, Chefe do Departamento de Pediatria do Hospital do Câncer.

DOI:

https://doi.org/10.32635/2176-9745.RBC.2000v46n3.2440

Keywords:

Primitive Neuroectodermic Tumor, Sarcoma, Soft Tissue Neoplasms

Abstract

Proposal: The autors review the chart of 13 patients with diagnosis of peripheral primitive neuroectodermal tumor (PNET), admitted at the Pediatric Department of Cancer Hospital between the period of 1989 and 1996. Patients and methods: All patients with PNET were analysed in a retrospective way, using epidemiologic clinical data, treatment and outcome. Results: Surgery was the first therapeutic approach in 2 patients. Chemotherapy was administered in 12 patient and radiotherapy in 2. From the 13 patient, five are alive with an average follow up of 48 months after the end of the treatment. Conclusion: This analyis confirms the heterogeneity and agressiveness of PNET tumors. Multicentric studies are necessary for prognostic factors analysis.

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Published

2000-09-29

How to Cite

1.
Costa CML, Rondinelli P, Camargo B de. Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review. Rev. Bras. Cancerol. [Internet]. 2000 Sep. 29 [cited 2024 Jul. 22];46(3):293-98. Available from: https://rbc.inca.gov.br/index.php/revista/article/view/2440

Issue

Vol. 46 No. 3 (2000): July/Aug./Sept.

Section

LITERATURE REVIEW

License

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.