Dermatofibrosarcoma protuberans metastático para pulmão - relato de caso

Authors

  • Nelson José Jabour Fiod Cirurgião Oncológico de Seção de Tecido Ósseo Conectivo (T.O.C). Instituto Nacional de Câncer (INCA). Rio de Janeiro (RJ), Brasil
  • José Francisco Neto Chefe da Seção de Tecido Ósseo Conectivo (T.O.C). Instituto Nacional de Câncer (INCA). Rio de Janeiro (RJ), Brasil
  • Carlos Guitmann Divisão de Cirurgia Oncológica. Instituto Nacional de Câncer (INCA). Rio de Janeiro (RJ), Brasil
  • Walter Meohas Seção de Tecido Ósseo Conectivo (T.O.C). Instituto Nacional de Câncer (INCA). Rio de Janeiro (RJ), Brasil
  • Rogério Estevan Patologista. Instituto Nacional de Câncer (INCA). Rio de Janeiro (RJ), Brasil

DOI:

https://doi.org/10.32635/2176-9745.RBC.1994v40n3.2989

Keywords:

Dermatofibrosarcoma, Dermatofibrosarcoma Protuberans Metastatic, Neoplasm Metastasis

Abstract

An unusual case of a metastasizing Dermatofibrosarcoma Protuberans is reported. The tumor metastasized to the lung 16 years after wide excision of the primary lesion. The clinicai and pathologic features of Dermatofibrosarcoma Protuberans are reviewed and treatment is discussed, with the aim of emphasizing the need for long term follow up wide excision of the lesions.

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References

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PATIL P. K., PATEL S. G., KRISHNAMURTHY S., MISTRY R. C., DESHPANDE R. K., DESAI P. B. Dermatofibrosarcoma Protuberans metastatic to the Lung. A case report. Tumori, 78: 49-51, 1992. DOI: https://doi.org/10.1177/030089169207800112

Published

2023-06-05

How to Cite

1.
Fiod NJJ, José Francisco Neto, Guitmann C, Meohas W, Estevan R. Dermatofibrosarcoma protuberans metastático para pulmão - relato de caso. Rev. Bras. Cancerol. [Internet]. 2023 Jun. 5 [cited 2024 May 20];40(3):169-73. Available from: https://rbc.inca.gov.br/index.php/revista/article/view/2989

Issue

Section

CASE REPORT

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